James Huang, MD

  1. A pilot trial of prophylactic defibrotide to prevent serious thrombotic microangiopathy in high-risk pediatric patients.
  2. Diagnostic work-up for severe aplastic anemia in children: Consensus of the North American Pediatric Aplastic Anemia Consortium.
  3. Plasma-derived factor X concentrate compassionate use for hereditary factor X deficiency: Long-term safety and efficacy in a retrospective data-collection study.
  4. Distinct genetic pathways define pre-malignant versus compensatory clonal hematopoiesis in Shwachman-Diamond syndrome.
  5. A study assessing the feasibility of randomization of pediatric and young adult patients between matched unrelated donor bone marrow transplantation and immune-suppressive therapy for newly diagnosed severe aplastic anemia: A joint pilot trial of the Nort
  6. Immunosuppressive therapy for pediatric aplastic anemia: a North American Pediatric Aplastic Anemia Consortium study.
  7. Low Exposure Busulfan Conditioning to Achieve Sufficient Multilineage Chimerism in Patients with Severe Combined Immunodeficiency.
  8. Investigation of Pediatric Anemia in the Commonwealth of the Northern Mariana Islands.
  9. Understanding the evolving phenotype of vascular complications in telomere biology disorders.
  10. Comprehensive Review of Preschool Age Anemia in the Pacific Island Jurisdictions.
  11. Capacity Building for Rare Bleeding Disorders in the Remote Commonwealth of the Northern Mariana Islands.
  12. Elevated tricuspid regurgitant jet velocity in subgroups of thalassemia patients: insight into pathophysiology and the effect of splenectomy.
  13. Diagnosis and treatment of pediatric acquired aplastic anemia (AAA): an initial survey of the North American Pediatric Aplastic Anemia Consortium (NAPAAC).
  14. Zinc supplementation improves bone density in patients with thalassemia: a double-blind, randomized, placebo-controlled trial.
  15. Re: 24-year-old man with previously diagnosed hemophilia.
  16. In vitro modeling of the microvascular occlusion and thrombosis that occur in hematologic diseases using microfluidic technology.
  17. Microenvironmental geometry guides platelet adhesion and spreading: a quantitative analysis at the single cell level.
  18. Functions of the mitotic B-type cyclins CLB1, CLB2, and CLB3 at mitotic exit antagonized by the CDC14 phosphatase.
  19. Pseudotumor of the mandible as first presentation of hemophilia in a 2-year-old male: a case report and review of jaw pseudotumors of hemophilia.
  20. Characterization of low bone mass in young patients with thalassemia by DXA, pQCT and markers of bone turnover.
  21. Clinical spectrum and molecular pathophysiology of Shwachman-Diamond syndrome.
  22. Guidelines for the management of spontaneous intracerebral hemorrhage: a guideline for healthcare professionals from the American Heart Association/American Stroke Association.
  23. Factor V deficiency: a concise review.
  24. Activity of the APC(Cdh1) form of the anaphase-promoting complex persists until S phase and prevents the premature expression of Cdc20p.
  25. Low-molecular-weight heparins.
  26. Selection and analysis of rare second-site suppressors of Drosophila RNA polymerase II mutations.
  27. APC-mediated proteolysis of Ase1 and the morphogenesis of the mitotic spindle.
  28. Surface hydrophobicity and water transport of the toad urinary bladder: effects of vasopressin.
  29. Antagonistic interactions between alleles of the RpII215 locus in Drosophila melanogaster.
  30. Monoamine oxidase: an important intracellular regulator of gastrin release in the rat.